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Taipei Medical University

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Gene Symbol
Gene NameAliasesPrevious_Symbol

CFTR

cystic fibrosis transmembrane conductance regulator, ATP-binding cassette (sub-family C, member 7)MRP7


Gene CFTR gene interaction
View Neighborhood Gene

Result number fewer <<<< << < ALL > >> >>> more

MeSH term
FrequencyCondition_Probility

Humans

7120.0

Female

1560.0

Middle Aged

490.0

Adolescent

690.0

Adult

1090.0

Child

700.0

Child, Preschool

460.0

Cystic Fibrosis Transmembrane Conductance Regulator/*genetics

13992.0

Forced Expiratory Volume

44.0

Genotype

740.0

Infant

380.0

Animals

2090.0

Cystic Fibrosis/metabolism/*therapy

375.0

Cystic Fibrosis Transmembrane Conductance Regulator/genetics/metabolism

857.0

Gene Expression

390.0

Gene Therapy/*methods

92.0

Genetic Vectors/*administration & dosage/genetics

318.0

Lentivirus/*genetics

37.0

Research Support, Non-U.S. Gov't

5470.0

Respiratory Mucosa/*metabolism

321.0

ATP-Binding Cassette Transporters/metabolism

36.0

Alleles

370.0

Amino Acid Motifs

70.0

Amino Acid Sequence

500.0

Blotting, Western

200.0

Cell Line

930.0

Cyclic AMP/metabolism

193.0

Dose-Response Relationship, Drug

210.0

Electrophoresis, Polyacrylamide Gel

140.0

Electrophysiology

255.0

Forskolin/pharmacology

318.0

Gene Deletion

150.0

Genetic Vectors

150.0

Genistein/pharmacology

32.0

Hela Cells

270.0

Models, Biological

130.0

Models, Genetic

40.0

Molecular Sequence Data

1300.0

Mutagenesis, Site-Directed

230.0

*Mutation

651.0

Phenylalanine/chemistry

26.0

Plasmids/metabolism

70.0

Protein Structure, Tertiary

170.0

Rats

390.0

Research Support, U.S. Gov't, P.H.S.

2760.0

Sequence Homology, Amino Acid

180.0

Transfection

730.0

Biological Transport, Active

52.0

Chlorides/metabolism

4346.0

Cystic Fibrosis Transmembrane Conductance Regulator/*drug effects

2100.0

Male

1850.0

Nasal Mucosa/physiopathology

5100.0

Cells, Cultured

550.0

Cystic Fibrosis Transmembrane Conductance Regulator/*chemistry/metabolism

4100.0

*Protein Folding

75.0

Adenocarcinoma

65.0

Cystic Fibrosis Transmembrane Conductance Regulator/*genetics/metabolism

1894.0

Forskolin/*pharmacology

517.0

Gene Expression Regulation/*drug effects

60.0

Genes, Reporter

100.0

Luciferases/genetics/metabolism

20.0

Lung Neoplasms

32.0

Promoter Regions (Genetics)

120.0

Recombinant Fusion Proteins/genetics/metabolism

30.0

Tetradecanoylphorbol Acetate/*pharmacology

30.0

Tumor Cells, Cultured

330.0

Cystic Fibrosis/genetics/metabolism

787.0

Cystic Fibrosis Transmembrane Conductance Regulator/genetics/*metabolism

4690.0

Dimerization

20.0

Electric Conductivity

2716.0

Ion Channel Gating/drug effects

210.0

Protein Binding

280.0

Sequence Deletion

170.0

Two-Hybrid System Techniques

20.0

*Gene Transfer Techniques

215.0

Green Fluorescent Proteins

30.0

Luminescent Proteins/genetics

21.0

Microscopy, Fluorescence

140.0

Organ Culture Techniques

30.0

Transgenes

61.0

CHO Cells

100.0

DNA, Complementary/metabolism

50.0

Endoplasmic Reticulum/metabolism

103.0

Glycosylation

202.0

Hamsters

290.0

Heat-Shock Proteins 70/metabolism

23.0

Immunohistochemistry

330.0

Kinetics

330.0

Molecular Chaperones/metabolism

24.0

Mutation

1051.0

Precipitin Tests

150.0

Protein Biosynthesis

40.0

Protein Conformation

150.0

Protein Folding

163.0

Time Factors

280.0

English Abstract

280.0

Gene Frequency

190.0

*Genetics, Population

30.0

Heterozygote

291.0

Introns

160.0

*Polymorphism, Genetic

90.0

*Alternative Splicing

50.0

Exons

270.0

Mice

1120.0

Sheep

30.0

Aged

210.0

Cystic Fibrosis/genetics/*metabolism

1381.0

Electrolytes/*metabolism

228.0

Homozygote

201.0

Osmolar Concentration

20.0

Species Specificity

120.0

Water-Electrolyte Balance

34.0

Binding, Competitive

30.0

Cell Membrane/metabolism

251.0

Cystic Fibrosis Transmembrane Conductance Regulator/*metabolism

4591.0

Exocytosis

34.0

Fluorescent Antibody Technique

80.0

Immunoblotting

140.0

Membrane Proteins/*metabolism

153.0

Reverse Transcriptase Polymerase Chain Reaction

260.0

Xenopus

142.0

Cystic Fibrosis/*therapy

1083.0

Epithelial Cells

153.0

RNA, Messenger/analysis

180.0

Transfection/methods

21.0

Binding Sites

180.0

Bronchoalveolar Lavage Fluid

24.0

*Gastrointestinal Hormones

330.0

Lung/cytology/*metabolism

26.0

Peptides/metabolism

20.0

Respiratory Mucosa/cytology/*metabolism

330.0

Signal Transduction

150.0

Comparative Study

580.0

Cystic Fibrosis/*epidemiology/*genetics

3100.0

Genetics, Population

41.0

Incidence

50.0

Infant, Newborn

220.0

Mutation/*genetics

231.0

Argentina

24.0

Cystic Fibrosis/diagnosis/*genetics

666.0

Genetic Heterogeneity

20.0

*Genetic Screening

42.0

Polymorphism, Genetic

210.0

Aged, 80 and over

70.0

Infertility, Male/*genetics

716.0

Vas Deferens/abnormalities

1392.0

Insects

21.0

Microscopy, Confocal

80.0

Oligonucleotides, Antisense/pharmacology

31.0

Peptides/chemistry

20.0

Protein Kinase C/*metabolism

62.0

Recombinant Proteins/metabolism

140.0

Cytosol/metabolism

40.0

Models, Molecular

110.0

Phosphorylation

330.0

Protein Structure, Secondary

70.0

Gene Therapy

226.0

Immunoenzyme Techniques

30.0

Mice, Inbred C57BL

120.0

Mice, Inbred CFTR

480.0

Nitric-Oxide Synthase/metabolism

21.0

Receptors, Cell Surface/*metabolism

30.0

beta-Galactosidase/genetics

32.0

Chlorides/*pharmacokinetics

2100.0

Ion Channel Gating/*drug effects

220.0

Membrane Potentials/drug effects

107.0

Patch-Clamp Techniques

4210.0

Cystic Fibrosis/diagnosis/*epidemiology/*genetics

2100.0

Genetic Screening

131.0

Pedigree

110.0

Phenotype

610.0

Residence Characteristics/statistics & numerical data

233.0

Restriction Mapping

80.0

Saudi Arabia/epidemiology

211.0

Microscopy, Fluorescence/*methods

215.0

Glutathione Transferase/metabolism

50.0

Nerve Tissue Proteins/metabolism

20.0

Recombinant Fusion Proteins/metabolism

60.0

Adenosine Triphosphate/pharmacology

68.0

Cystic Fibrosis Transmembrane Conductance Regulator/chemistry/*metabolism

7100.0

Models, Chemical

41.0

Potassium Channels/metabolism

411.0

Analysis of Variance

30.0

Lung/physiopathology

623.0

Cohort Studies

50.0

Cystic Fibrosis/*diagnosis/*genetics

583.0

Cystic Fibrosis Transmembrane Conductance Regulator/analysis/*genetics

6100.0

Genetic Markers

50.0

Italy

50.0

Neonatal Screening

26.0

*Phenotype

31.0

Sensitivity and Specificity

70.0

Bicarbonates/*metabolism

844.0

Cystic Fibrosis/metabolism

2374.0

Cystic Fibrosis Transmembrane Conductance Regulator/physiology

6100.0

Lung/metabolism/physiopathology

3100.0

Mucus/*secretion

220.0

Cystic Fibrosis Transmembrane Conductance Regulator/genetics/physiology

3100.0

Disease Models, Animal

120.0

Gene Transfer Techniques/adverse effects

2100.0

Cystic Fibrosis Transmembrane Conductance Regulator/*physiology

2095.0

Hydrogen-Ion Concentration

110.0

Permeability

53.0

Research Support, U.S. Gov't, Non-P.H.S.

220.0

Chlorides/*physiology

250.0

Cystic Fibrosis Transmembrane Conductance Regulator/genetics/*physiology

1292.0

Base Sequence

700.0

Blotting, Northern

90.0

Cloning, Molecular

120.0

Cystic Fibrosis/*metabolism

2655.0

Epithelial Cells/metabolism

175.0

In Situ Hybridization

180.0

Lung/metabolism

84.0

Mucins/metabolism

24.0

RNA, Messenger/metabolism

260.0

Up-Regulation

30.0

Cyclic AMP-Dependent Protein Kinases/metabolism

157.0

Cytochalasin D/pharmacology

33.0

Cyclic AMP-Dependent Protein Kinases/*metabolism

77.0

4,4'-Diisothiocyanostilbene-2,2'-Disulfonic Acid/pharmacology

830.0

Biological Transport/drug effects/physiology

515.0

Enzyme Inhibitors/pharmacology

130.0

Nitric Oxide Donors/pharmacology

23.0

Thapsigargin/pharmacology

21.0

ATP-Binding Cassette Transporters/*metabolism

22.0

Adenosine Triphosphate/*metabolism

1314.0

Diffusion

44.0

Carrier Proteins/*genetics/metabolism

20.0

Chromosomes, Human, Pair 7

42.0

Gene Expression Regulation

180.0

In Situ Hybridization, Fluorescence

50.0

*Transcription, Genetic

80.0

Down-Regulation

60.0

Ion Transport/drug effects

719.0

Nasal Mucosa/metabolism/pathology

233.0

Nasal Polyps/*metabolism/pathology

216.0

*Gene Expression Regulation

70.0

RNA, Messenger

20.0

Tissue Distribution

150.0

Chlorides/*analysis

2100.0

Double-Blind Method

70.0

Membrane Potentials

2713.0

Multicenter Studies

21.0

Randomized Controlled Trials

20.0

Reproducibility of Results

50.0

Sweat/*chemistry

375.0

Cystic Fibrosis/genetics

2066.0

Oligospermia/genetics

211.0

Risk Factors

60.0

Vas Deferens/*abnormalities

2295.0

Chloride Channels/drug effects/*physiology

360.0

Codon

20.0

Cyclic AMP/pharmacology

1816.0

Cyclic AMP-Dependent Protein Kinases/pharmacology

436.0

Cystic Fibrosis/*physiopathology

323.0

Ionomycin/pharmacology

41.0

Chronic Disease

181.0

Genetic Predisposition to Disease/genetics

20.0

*Trypsin

518.0

Trypsin Inhibitor, Kazal Pancreatic/genetics

266.0

Trypsinogen/genetics

444.0

Cystic Fibrosis/complications/*diagnosis/genetics

2100.0

Cystic Fibrosis Transmembrane Conductance Regulator/genetics

4263.0

Diagnosis, Differential

50.0

European Continental Ancestry Group/*genetics

20.0

Prevalence

60.0

Recurrence

30.0

Cystic Fibrosis/*complications

342.0

Lung Diseases/genetics

250.0

Mutation/*physiology

43.0

Cystic Fibrosis/*genetics

8080.0

Epithelium/metabolism

338.0

*Genetic Predisposition to Disease

20.0

Ion Transport

1420.0

Pancreatitis/*genetics

617.0

Sweat/metabolism

350.0

Clinical Trials

50.0

*Gene Therapy

164.0

Nasal Mucosa

240.0

Rabbits

170.0

Safety

21.0

Structure-Activity Relationship

130.0

Treatment Outcome

50.0

DNA/genetics

100.0

DNA Primers

160.0

Genes, Structural

40.0

Polymerase Chain Reaction

590.0

Sequence Analysis, DNA

100.0

Autistic Disorder/*genetics

23.0

Carrier Proteins/*genetics

40.0

Chromosomes, Human, Pair 7/*genetics

32.0

DNA Mutational Analysis

270.0

DNA, Complementary/chemistry/genetics

20.0

Genetic Predisposition to Disease

50.0

Nerve Tissue Proteins/*genetics

20.0

Point Mutation

90.0

RNA, Messenger/genetics/metabolism

60.0

Sequence Alignment

130.0

Calcium/metabolism

60.0

Intestinal Absorption

21.0

Mice, Knockout

90.0

Cystic Fibrosis Transmembrane Conductance Regulator/*biosynthesis

2100.0

Adenosine Triphosphate/metabolism

153.0

Biological Transport

161.0

Cysteine Endopeptidases/*metabolism

20.0

Glycerol/pharmacology

218.0

In Vitro

290.0

Leupeptins/pharmacology

32.0

Lipid Bilayers/metabolism

725.0

Multienzyme Complexes/*metabolism

21.0

Proteasome Endopeptidase Complex

71.0

Trypsin/pharmacology

21.0

Ubiquitins/metabolism

21.0

Chile

23.0

Caco-2 Cells

51.0

Chloride Channels/analysis/*physiology

2100.0

Chlorides/*metabolism

3044.0

Intestinal Mucosa/*metabolism

56.0

*Evolution

21.0

Nutritional Status

42.0

Cell Division

30.0

Cytoskeleton/metabolism

20.0

Amiloride/pharmacology

1029.0

Chloride Channels/antagonists & inhibitors

240.0

Cystic Fibrosis Transmembrane Conductance Regulator/metabolism

758.0

Mice, Inbred Strains

40.0

Thionucleotides/pharmacology

58.0

Kidney/metabolism

30.0

1-Methyl-3-isobutylxanthine/pharmacology

88.0

Dogs

90.0

Phosphodiesterase Inhibitors/pharmacology

76.0

Pulmonary Circulation/physiology

225.0

Amino Acid Substitution

30.0

Bronchi/cytology/metabolism

213.0

Oocytes/metabolism

73.0

Sodium/metabolism

96.0

Sodium Channels/genetics/*metabolism

541.0

Xenopus laevis

184.0

DNA/chemistry/genetics

20.0

Mutation, Missense

50.0

*Phylogeny

21.0

Sequence Homology, Nucleic Acid

80.0

Adenoviridae/*genetics

62.0

DNA, Recombinant

21.0

Transduction, Genetic

41.0

*Transfection

72.0

Gene Therapy/adverse effects/*methods

228.0

Genetic Vectors/*administration & dosage

28.0

Tomography, X-Ray Computed

20.0

DNA/metabolism

40.0

Oligonucleotides/metabolism

22.0

RNA/metabolism

20.0

Ultraviolet Rays

30.0

ATP-Binding Cassette Transporters/*genetics

20.0

*Gene Expression

111.0

Multidrug Resistance-Associated Proteins

22.0

Body Height

42.0

Body Weight

40.0

Europe

20.0

*Homozygote

53.0

Mutation/genetics

131.0

Predictive Value of Tests

30.0

Prognosis

40.0

Registries

20.0

Acute Disease

30.0

Exons/genetics

80.0

Introns/genetics

40.0

*Polymorphism, Single-Stranded Conformational

32.0

Chromosomes, Artificial, Yeast

20.0

DNA-Binding Proteins/metabolism

30.0

Deoxyribonuclease I/metabolism

42.0

*Introns

73.0

Mice, Transgenic

180.0

*Regulatory Sequences, Nucleic Acid

30.0

Transcription, Genetic

180.0

Cystic Fibrosis Transmembrane Conductance Regulator/analysis/*metabolism

2100.0

Gene Expression/physiology

30.0

Signal Transduction/physiology

30.0

Enzyme Activation

50.0

*Alleles

80.0

Lymphocytes

21.0

Pregnancy

90.0

Adenosine Triphosphate/*blood

225.0

Pancreas/*metabolism

25.0

RNA, Messenger/*analysis

40.0

Molecular Weight

30.0

Point Mutation/genetics

31.0

Thermodynamics

30.0

Nucleic Acid Hybridization

50.0

Sequence Analysis, DNA/*methods

34.0

Chromosome Mapping

80.0

Genome

20.0

Microsatellite Repeats

40.0

Oocytes

1211.0

DNA Primers/chemistry

60.0

Membrane Proteins/biosynthesis/*genetics

511.0

RNA, Messenger/*biosynthesis

31.0

Cysteine Endopeptidases

24.0

Isoxazoles/pharmacology

213.0

Multienzyme Complexes/antagonists & inhibitors

27.0

Protein Processing, Post-Translational/*drug effects

23.0

Protein Synthesis Inhibitors/pharmacology

30.0

Epithelial Cells/*metabolism

43.0

Trans-Activation (Genetics)

40.0

beta-Galactosidase/metabolism

21.0

Crystallization

20.0

Ligands

30.0

Protein Structure, Quaternary

21.0

Substrate Specificity

30.0

RNA, Messenger/analysis/genetics

40.0

Syndrome

30.0

Transgenes/genetics

33.0

Fluorescent Dyes/metabolism

22.0

Tumor Necrosis Factor-alpha/pharmacology

20.0

Chloride Channels/metabolism

1477.0

Isoproterenol/pharmacology

98.0

Cyclic AMP/analogs & derivatives/pharmacology

225.0

Membrane Potentials/drug effects/physiology

1013.0

Oocytes/physiology

65.0

Protein Kinase C/metabolism

61.0

Protein Transport/drug effects/physiology

210.0

Homeostasis

41.0

Pancreatic Ducts/*metabolism

266.0

Phylogeny

50.0

Recombinant Proteins/chemistry/metabolism

50.0

Survival Analysis

40.0

Recombinant Proteins/genetics/metabolism

71.0

DNA, Satellite/*genetics

23.0

Haplotypes

80.0

Linkage (Genetics)

40.0

Sodium-Potassium-Chloride Symporters

215.0

DNA

90.0

Polymerase Chain Reaction/methods

90.0

Preimplantation Diagnosis/*methods

211.0

Sweat Glands/*metabolism

466.0

Golgi Apparatus/metabolism

42.0

Microscopy, Immunoelectron

20.0

3T3 Cells

120.0

Cell Line, Tumor

30.0

Repressor Proteins/*physiology

21.0

Organ Specificity

50.0

Cyclic AMP/*physiology

78.0

GTP-Binding Proteins/*physiology

21.0

Guanosine 5'-O-(3-Thiotriphosphate)/pharmacology

34.0

Biological Transport/physiology

31.0

Chlorides/antagonists & inhibitors/*metabolism

3100.0

Mutation/physiology

54.0

Reference Values

70.0

Trachea/cytology/*metabolism

218.0

Cystic Fibrosis/ethnology/*genetics

4100.0

DNA Mutational Analysis/*methods

43.0

Genetic Screening/methods

32.0

Na(+)-K(+)-Exchanging ATPase/metabolism

24.0

Sodium Channels/metabolism

350.0

Nasal Mucosa/*metabolism

631.0

Carrier Proteins/genetics/*metabolism

20.0

*Ligases

21.0

Multienzyme Complexes/antagonists & inhibitors/*metabolism

29.0

Protein Structure, Tertiary/physiology

31.0

*Ubiquitin-Protein Ligases

30.0

Gene Expression Regulation/*physiology

20.0

Polymorphism, Restriction Fragment Length

60.0

Smoking

20.0

Cystic Fibrosis/genetics/*metabolism/physiopathology

266.0

Gene Frequency/genetics

20.0

Drug Synergism

20.0

Rats, Inbred F344

30.0

Cell Line, Transformed

80.0

Fetus

40.0

Hydrogen Peroxide/pharmacology

31.0

Pigment Epithelium of Eye/cytology/drug effects/*metabolism

218.0

Age of Onset

20.0

Lung Diseases/*genetics

220.0

Sweat/chemistry/secretion

2100.0

Gene Library

30.0

Oligonucleotide Probes/genetics

21.0

Diuretics/pharmacology

330.0

Stilbenes/pharmacology

39.0

Swine

40.0

Tetrodotoxin/pharmacology

25.0

Vasoactive Intestinal Peptide/pharmacology

22.0

Adenylyl Imidodiphosphate/pharmacology

466.0

Hydrolysis

81.0

Magnesium/pharmacology

32.0

Interleukin-1/metabolism

20.0

Mice, Inbred BALB C

30.0

Pseudomonas aeruginosa/physiology

233.0

*Genotype

20.0

Sodium Channels/*physiology

330.0

Gene Dosage

20.0

*Prenatal Diagnosis

31.0

Age Factors

70.0

Cystic Fibrosis Transmembrane Conductance Regulator/*analysis

2100.0

Fluorescent Antibody Technique, Indirect

60.0

Multigene Family

20.0

Drug Resistance, Multiple

21.0

Polymorphism, Single-Stranded Conformational

70.0

Chromosome Deletion

40.0

France/epidemiology

32.0

Infertility, Male/epidemiology/genetics

2100.0

Mutation, Missense/genetics

21.0

Polymorphism, Genetic/genetics

60.0

Bacterial Adhesion

34.0

Epithelium/chemistry

43.0

Liposomes

72.0

Phosphatidylethanolamines

211.0

Cystic Fibrosis/*metabolism/pathology

225.0

Liver/*chemistry

25.0

Anions/*metabolism

350.0

Anthranilic Acids/pharmacology

360.0

Calcium Channel Blockers/pharmacology

33.0

Glyburide/pharmacology

526.0

Nitrobenzoates/pharmacology

222.0

Nystatin/pharmacology

216.0

Sodium Channels/*metabolism

419.0

Karyotyping

30.0

*Linkage (Genetics)

20.0

*Amino Acid Transport Systems, Basic

25.0

*Bacterial Proteins

21.0

Membrane Proteins/metabolism

61.0

Gene Transfer Techniques

101.0

*Genetic Vectors

144.0

Prospective Studies

50.0

Severity of Illness Index

40.0

Kidney/abnormalities

210.0

*Mutation/genetics

26.0

*Variation (Genetics)

20.0

Cyclic AMP/physiology

65.0

Gene Expression Regulation/physiology

20.0

Membrane Proteins/genetics

102.0

*DNA Mutational Analysis

31.0

Genetic Predisposition to Disease/*genetics

30.0

Pancreatitis/diagnosis/*genetics

233.0

Testis/metabolism

20.0

Frameshift Mutation

30.0

Heteroduplex Analysis

22.0

Gene Therapy/methods

33.0

Ethnic Groups/genetics

21.0

Alternative Splicing/genetics

31.0

Enhancer Elements (Genetics)

30.0

Exons/*genetics

41.0

RNA, Messenger/genetics

130.0

Transcription, Genetic/genetics

20.0

Cell Compartmentation

41.0

Endocytosis/drug effects

23.0

Chloride Channels/physiology

466.0

Ion Channel Gating

1318.0

Arginine/genetics

31.0

*Gene Deletion

30.0

Oligospermia/diagnosis/genetics

2100.0

Protein Processing, Post-Translational/genetics

210.0

Conserved Sequence

20.0

Cystic Fibrosis Transmembrane Conductance Regulator/*genetics/*metabolism

8100.0

*Exons

92.0

Gene Amplification

20.0

Repetitive Sequences, Nucleic Acid

20.0

Vas Deferens/*abnormalities/metabolism

2100.0

Interleukin-8/metabolism

21.0

Trypsin/metabolism

32.0

Cystic Fibrosis/complications/*genetics

480.0

Temperature

60.0

Chloride Channels/drug effects

466.0

*Mutation, Missense

30.0

Anti-Inflammatory Agents/therapeutic use

22.0

Cystic Fibrosis/*genetics/*physiopathology/therapy

2100.0

Anions/metabolism

842.0

Anti-Inflammatory Agents, Non-Steroidal/*pharmacology

21.0

Cell Survival/drug effects

20.0

Recombinant Proteins/biosynthesis

40.0

RNA, Messenger/*metabolism

20.0

Respiratory System/*metabolism

214.0

Tumor Cells, Cultured/drug effects/metabolism/pathology

25.0

Carrier Proteins/*metabolism

20.0

*Genes, Structural

30.0

Mice/*genetics

20.0

Regulatory Sequences, Nucleic Acid

40.0

Base Sequence/genetics

20.0

Molecular Conformation

31.0

Membrane Proteins/genetics/*metabolism

93.0

Cell Membrane/*metabolism

20.0

Light

20.0

Protein Transport

60.0

Bronchi/*metabolism

39.0

Protein Structure, Tertiary/genetics

31.0

Staining and Labeling

20.0

*Tumor Suppressor Proteins

20.0

Exocrine Pancreatic Insufficiency/genetics

2100.0

Chlorides/pharmacokinetics

250.0

Sodium/pharmacokinetics

266.0

Phosphoprotein Phosphatase/metabolism

22.0

Cell Membrane Permeability

63.0

Sodium Chloride/metabolism

216.0

RNA, Messenger/*biosynthesis/genetics

23.0

Cystic Fibrosis/complications/*genetics/physiopathology

2100.0

Genetic Complementation Test

50.0

Asthma/*genetics

23.0

Fibroblasts/metabolism

20.0

Lung/*metabolism

44.0

Magnetic Resonance Spectroscopy

20.0

Oligosaccharides/metabolism

24.0

Spectrometry, Mass, Fast Atom Bombardment

27.0

alpha-L-Fucosidase/genetics/metabolism

2100.0

Cystic Fibrosis Transmembrane Conductance Regulator/chemistry/*genetics

3100.0

Electrophoresis, Agar Gel

40.0

Nucleic Acid Conformation

40.0

Epithelial Cells/physiology

34.0

Recombinant Fusion Proteins/chemistry/metabolism

21.0

*Sodium-Hydrogen Antiporter

327.0

Bronchi

216.0

Colon

27.0

*Meconium

266.0

Retrospective Studies

60.0

*Ion Channel Gating

212.0

Respiratory System/cytology/*metabolism

225.0

Adenovirus E4 Proteins/*genetics

250.0

Variation (Genetics)

100.0

Cystic Fibrosis/*genetics/*therapy

375.0

Dependovirus/*genetics

33.0

*Promoter Regions (Genetics)

70.0

DNA, Complementary/analysis/genetics

22.0

Lipids

315.0

Nasal Mucosa/metabolism

327.0

Chromatography, High Pressure Liquid/methods

21.0

Proteins/genetics

30.0

Repressor Proteins/genetics

21.0

Recombinant Proteins/biosynthesis/metabolism

21.0

*Sequence Deletion

82.0

DNA Footprinting

31.0

Deoxyribonuclease I/*metabolism

211.0

Kidney/cytology/*metabolism

29.0

Nitroso Compounds/pharmacology

211.0

Heterozygote Detection

61.0

Dinucleotide Repeats/genetics

24.0

Cell Polarity

21.0

Tetradecanoylphorbol Acetate/pharmacology

30.0

Alkaline Phosphatase/genetics/metabolism

211.0

Bronchi/cytology/*metabolism

321.0

Cation Exchange Resins

222.0

Drug Carriers

21.0

*Liposomes

25.0

Transfection/*methods

35.0

Mucus/secretion

225.0

Electrophoresis, Capillary

24.0

Chloride Channels/*physiology

555.0

Case-Control Studies

60.0

Cystic Fibrosis/*genetics/metabolism

5100.0

Intestines/metabolism

43.0

Respiratory System/metabolism

330.0

Sweat Glands/metabolism

228.0

Antibodies/pharmacology

20.0

*Sodium Channel Blockers

222.0

DNA, Complementary/*administration & dosage

225.0

Cystic Fibrosis Transmembrane Conductance Regulator/*analysis/genetics

3100.0

Glyceraldehyde-3-Phosphate Dehydrogenases/analysis/genetics

2100.0

Keratin/analysis

20.0

Myocardium/*metabolism

41.0

RNA, Complementary/genetics

222.0

Recombinant Proteins/chemistry/genetics/metabolism

20.0

Isoenzymes/metabolism

20.0

Lysophosphatidylcholines/metabolism

215.0

Phospholipases A/*metabolism

24.0

Photoaffinity Labels

212.0

*Potassium Channels, Inwardly Rectifying

36.0

Heat-Shock Proteins/*metabolism

23.0

Pancreatic Neoplasms

25.0

Transcription Factors/metabolism

40.0

Chloride Channels/*metabolism

323.0

Genetic Counseling

21.0

COS Cells

80.0

Epithelial Cells/microbiology

28.0

Flow Cytometry

20.0

Inflammation

20.0

Lung/metabolism/*physiopathology

2100.0

Cystic Fibrosis Transmembrane Conductance Regulator/chemistry/*physiology

2100.0

Ion Channels/*metabolism

24.0

Italy/epidemiology

20.0

DNA, Complementary/genetics

90.0

Adrenergic beta-Agonists/pharmacology

48.0

Colon/drug effects/metabolism

228.0

Epithelium/drug effects/metabolism

23.0

Kidney

30.0

*Point Mutation

120.0

Genistein/*pharmacology

39.0

Cytosol/*metabolism

26.0

Endoplasmic Reticulum/*metabolism

21.0

DNA Mutational Analysis/*standards

240.0

Quality Control

42.0

Lung/*metabolism/pathology

29.0

*Heterozygote

20.0

Transcription Factors/genetics

20.0

Membrane Potentials/physiology

55.0

DNA-Binding Protein, Cyclic AMP-Responsive/*metabolism

22.0

Oxazoles/pharmacology

25.0

Xanthines/pharmacology

212.0

Chlorides/analysis/metabolism

2100.0

DNA/analysis

70.0

Epithelium/physiopathology

266.0

Follow-Up Studies

20.0

Sweat/chemistry

880.0

Gene Expression/drug effects

30.0

Biological Transport/drug effects

20.0

Potassium/metabolism

65.0

Genetic Engineering

22.0

Microscopy, Electron

60.0

Plasmids

90.0

Pseudomonas aeruginosa/*physiology

240.0

Adenoviridae/genetics

51.0

Tumor Necrosis Factor-alpha/*pharmacology

20.0

RNA Splicing/genetics

32.0

Mutagenesis, Insertional/*genetics

26.0

Sequence Deletion/*genetics

21.0

Antibody Specificity

20.0

Enzyme-Linked Immunosorbent Assay

30.0

*Membrane Proteins

20.0

Calcium/pharmacology

31.0

*Bacterial Adhesion

24.0

Cell Nucleus/metabolism

20.0

Protease Inhibitors/pharmacology

31.0

Trachea/*metabolism

423.0

Cystic Fibrosis/*genetics/physiopathology

1184.0

*Saccharomyces cerevisiae Proteins

20.0

Colon/microbiology

240.0

Epithelium/microbiology

29.0

Recombinant Proteins

81.0

Peptide Hydrolases/metabolism

21.0

Protein Processing, Post-Translational

40.0

Oligospermia/*genetics

510.0

Fluorescence

41.0

Cattle

50.0

Cell Transplantation

22.0

Transplantation, Heterologous

40.0

Chromatography, High Pressure Liquid/*methods

32.0

Evaluation Studies

20.0

Nucleic Acid Denaturation

33.0

Proto-Oncogene Proteins/genetics

20.0

Intestine, Small/metabolism

35.0

RNA, Messenger/biosynthesis

30.0

Xanthines/*pharmacology

342.0

Spodoptera

41.0

Escherichia coli/genetics

30.0

Recombinant Fusion Proteins/chemistry/genetics/metabolism

31.0

Microscopy, Fluorescence/methods

26.0

Vasoactive Intestinal Peptide/*pharmacology

22.0

DNA, Single-Stranded

33.0

Promoter Regions (Genetics)/genetics

20.0

Endopeptidases/*metabolism

32.0

Microsomes/metabolism

32.0

Peptide Mapping

40.0

Chlorides/analysis

350.0

Nasal Cavity/physiopathology

266.0

*Chromosome Mapping

20.0

DNA, Complementary

80.0

Hybrid Cells

40.0

Epithelium/physiology

67.0

Lac Operon

21.0

*Genetic Markers

20.0

Adenoviridae

22.0

Chlorides/physiology

360.0

Codon, Terminator

23.0

Diphosphates/pharmacology

266.0

Lipid Bilayers

614.0

Autoradiography

20.0

Cystic Fibrosis Transmembrane Conductance Regulator/biosynthesis/genetics

266.0

Drug Resistance, Multiple/*genetics

23.0

Image Processing, Computer-Assisted

41.0

Rats, Sprague-Dawley

30.0

Vas Deferens/*chemistry

2100.0

Antibodies, Monoclonal

30.0

Cell Differentiation

20.0

RNA-Directed DNA Polymerase

21.0

Genetic Vectors/genetics

41.0

Lac Operon/genetics

27.0

Biological Markers

20.0

Biopsy

20.0

Cytoskeletal Proteins/metabolism

20.0

Carbachol/pharmacology

22.0

Chromosomes, Artificial, Yeast/genetics

21.0

Pancreatic Ducts/metabolism

342.0

Recombination, Genetic

50.0

Cystic Fibrosis/*pathology

2100.0

Pregnancy Trimester, Second

20.0

*Chromosomes, Artificial, Yeast

23.0

Bacterial Adhesion/*physiology

29.0

Liposomes/chemistry

215.0

Microscopy, Electron, Scanning

20.0

DNA/*analysis

20.0

Collagen/genetics

22.0

Nephritis, Hereditary/genetics

225.0

Silver Staining

22.0

Cyclic AMP/*pharmacology

47.0

Phosphoric Monoester Hydrolases/antagonists & inhibitors

218.0

5' Untranslated Regions/genetics

21.0

Sequence Deletion/genetics

31.0

Prenatal Diagnosis

21.0

Gene Expression Regulation/genetics

21.0

Sodium/*metabolism

34.0

Transformation, Genetic

21.0

European Continental Ancestry Group/genetics

20.0

Ion Channels/*physiology

26.0

Cystic Fibrosis/epidemiology/*genetics

8100.0

Chloride Channels/drug effects/*metabolism

266.0

Guinea Pigs

20.0

Gene Expression/genetics

31.0

RNA Processing, Post-Transcriptional

21.0

Mutagenesis

50.0

Probability

20.0

Cell Membrane/physiology

42.0

Defective Viruses/genetics

213.0

Epithelium

46.0

Ion Channels/drug effects/*metabolism

250.0

Consensus Sequence

30.0

*Sequence Tagged Sites

25.0

Pancreas/physiopathology

555.0

Immunohistochemistry/*methods

22.0

Ion Channel Gating/physiology

313.0

Protein Kinases/metabolism

71.0

Blotting, Southern

30.0

Endosomes/metabolism

21.0

Models, Structural

21.0

*Protein Structure, Secondary

21.0

Centrifugation, Density Gradient

30.0

Ion Transport/genetics

440.0

Trachea/metabolism

422.0

Cyclic AMP/*metabolism

104.0

*Antiporters

28.0

Cycloheximide/pharmacology

20.0

Chloride Channels/analysis/*metabolism

2100.0

DNA Primers/genetics

30.0

Macaca fascicularis

20.0

Animals, Newborn

20.0

Gene Targeting

20.0

Meconium

233.0

Single-Blind Method

20.0

Membrane Proteins/metabolism/*physiology

26.0

*Disease Models, Animal

20.0

Intracellular Membranes/metabolism

21.0

Oligodeoxyribonucleotides

60.0

Spectrometry, Fluorescence

20.0

Genetic Vectors/*genetics

34.0

DNA Probes

30.0

Photochemistry

23.0

Genes

20.0

Molecular Probes/genetics

22.0

Vas Deferens/physiopathology

2100.0

Mice, Nude

20.0

Sulfates/metabolism

23.0

Sulfur Radioisotopes

22.0

Recombinant Proteins/biosynthesis/chemistry/metabolism

22.0

Iodides/metabolism

218.0

Genes, Regulator/*genetics

37.0

Fluorescent Dyes

30.0

Cystic Fibrosis Transmembrane Conductance Regulator

13391.0

Membrane Proteins/*genetics

435.0

Methylation

30.0

Chloride Channels/biosynthesis

375.0

Membrane Proteins/*biosynthesis/genetics

25.0

Recombinant Proteins/biosynthesis/drug effects/metabolism

2100.0

Absorption

21.0

Catalysis

20.0

Chloride Channels/genetics

216.0

*Fertilization in Vitro

21.0

Spermatozoa/*physiology

25.0

Membrane Proteins/*genetics/metabolism

53.0

Action Potentials

23.0

*Cystic Fibrosis

3100.0

*Polymerase Chain Reaction

31.0

DNA/*genetics

51.0

Bronchiectasis/*genetics

250.0

RNA/analysis

20.0

*RNA Splicing

72.0

Cystic Fibrosis/genetics/*therapy

3100.0

Membrane Proteins/genetics/physiology

28.0

Chloride Channels/*genetics

47.0

Sodium/metabolism/pharmacokinetics

2100.0

Pseudomonas aeruginosa/*pathogenicity

220.0

Cystic Fibrosis/*genetics/*physiopathology

2100.0

Dystrophin/genetics

211.0

*Genetic Techniques

46.0

Oligonucleotide Probes

20.0

Transcription, Genetic/drug effects

30.0

Phosphoproteins/chemistry

28.0

Membrane Proteins/*genetics/*physiology

214.0

Drug Resistance

20.0

Membrane Glycoproteins/*genetics

20.0

P-Glycoprotein

24.0

Fetus/*metabolism

22.0

Membrane Proteins/immunology/*metabolism

27.0

Nucleotides/metabolism

38.0

Membrane Proteins/*genetics/physiology

415.0

*Endocytosis

21.0

Dactinomycin/pharmacology

20.0

Transferrin/metabolism

21.0

*Genes, Regulator

21.0

Antisense Elements (Genetics)

23.0

Colon/*metabolism

47.0

Intestine, Small/*metabolism

27.0

RNA Probes

21.0

*Chromosomes, Human, Pair 7

20.0

Colonic Neoplasms

53.0

Immunosorbent Techniques

20.0

Membrane Proteins/chemistry/*genetics

23.0

DNA/genetics/isolation & purification

31.0

L Cells (Cell Line)

31.0

Membrane Proteins/genetics/*physiology

35.0

Chloride Channels

1368.0

X Chromosome

20.0

Baculoviridae/genetics

21.0

Exocytosis/physiology

28.0

Ion Channels/metabolism

415.0

Cyclic GMP/pharmacology

211.0

Membrane Proteins/*physiology

21.0

Protein Kinases/*metabolism

20.0

ATP-Binding Cassette Transporters/genetics

23.0

*ATP-Binding Cassette Transporters

21.0

Iodides/pharmacology

225.0

Cystic Fibrosis/*genetics/metabolism/physiopathology

2100.0

Protein Isoforms/genetics/metabolism

21.0

*Chromosome Deletion

30.0

RNA, Messenger/*genetics/metabolism

34.0

Lymphocytes/physiology

22.0

Cystic Fibrosis/*diagnosis/epidemiology

2100.0

Linkage (Genetics)/genetics

20.0

Plasmids/genetics

20.0

Trachea

27.0

African Continental Ancestry Group/genetics

20.0

RNA Splicing

30.0

RNA, Messenger/genetics/isolation & purification

35.0

Respiratory Mucosa/*physiology

342.0

Germany

20.0

Chlorides/chemistry

2100.0

Databases, Genetic

22.0

United States

20.0

Serine Proteinase Inhibitors/genetics

222.0

NF-kappa B/metabolism

30.0

Quinolizines/*pharmacology

2100.0

Enzyme Activation/physiology

21.0

Oxidants/pharmacology

23.0

Trypsin Inhibitor, Kazal Pancreatic/*genetics

210.0

Nucleic Acid Amplification Techniques/methods

216.0

*Vesicular Transport Proteins

21.0

Ion Transport/*genetics

250.0

Phosphoproteins/metabolism

20.0

*Neonatal Screening

28.0

Genetic Predisposition to Disease/epidemiology

22.0

Ion Transport/*physiology

266.0

Respiratory Mucosa/drug effects/*physiology

233.0

Electrophysiology/methods

213.0